Avaliação morfométrica do quadril de crianças e adolescentes com Doença Falciforme

Abstract

Sickle Cell Disease (SCD) is a hemoglobinopathy prevalent among individuals of African descent and is frequently associated with osteoarticular complications such as osteonecrosis (ON) of the femoral head. This cross-sectional study describes the hip morphology in children and adolescents with ON secondary to SCD, using radiographic indices: acetabular index (AI), Sharp angle, Wiberg angle, and cervicodiaphyseal angle. The muscle strength of participants was assessed using the MRC scale. Thirteen participants aged between 8 and 14 years were included in the study, resulting in the evaluation of 17 hips. Most hips showed AI within satisfactory values, with only one case classified as good. Both the Sharp angle and the cervicodiaphyseal angle demonstrated altered values suggesting hip dysplasia and coxa valga. Most hips showed satisfactory values for the Wiberg angle, with one hip considered unsatisfactory. Muscle strength was symmetrical and satisfactory, with no correlation to radiographic parameters or other variables. This study emphasizes the importance of early and continuous evaluation of hip morphology in young patients with SCD for the effective diagnosis and management of ON.