Resumo:
Introducion: Most of autoimmune rheumatic diseases present a chronic evolution, marked by
periods of remission and exacerbation of clinical manifestations. A striking feature is the
exposure of patients to medications with a high impact on quality of life. In Bahia, studies of
the prevalence of autoimmune rheumatic diseases are scarce, making it necessary to have an
overview of the profile of these diseases in the State. Objectives: Describe the demographic,
clinical, laboratory and therapeutic characteristics of children and adolescents with autoimmune
rheumatic diseases in a referral outpatient clinic of SUS in Pediatric Rheumatology of Salvador Bahia. Methodology: This is a retrospective cross-sectional study with a convenience sample
of children and adolescents from this clinic between December 2009 and December 2016 at the
Pediatric Rheumatology outpatient clinic, including diagnoses of juvenile idiopathic arthritis,
Juvenile systemic lupus erythematosus, rheumatic fever, juvenile dermatomyositis, juvenile
scleroderma and mixed connective tissue diseases. The data were obtained secondary, through
a review of medical records. Results: In a total of 169 patients with a confirmed diagnosis of
autoimmune rheumatic disease, 75 were diagnosed with juvenile idiopathic arthritis, 31 with
juvenile systemic lupus erythematosus, 42 with rheumatic fever, 11 with juvenile
dermatomyositis, 06 with juvenile scleroderma, and 04 with mixed connective tissue diseases.
The majority of the patients were female (59.2%), and brown patients (58.4%) and 71% of these
patients were not from Salvador. Low hemoglobin, low hematocrit and high HSV were the
main laboratory abnormalities observed. The most used drug therapy were
immunosuppressants, mainly methotrexate, followed by corticosteroids and non-hormonal
aintinflamatorios Discussion: The pediatric rheumatology services accompany children and
adolescents with various diseases and diverse prognoses. In the pediatric rheumatology
department of this study, less than half of the patients (32%) were included in the study because
of institutional limitations such as lack of access to medical records, lack of diagnostic
confirmation in a timely manner for insertion of the data, or confirmed diagnosis of other
Diseases. Conclusion: The majority of the patients attending the Pediatric Rheumatology
Outpatient Clinic accredited to the SUS in Salvador-BA with a diagnosis of autoimmune
rheumatic disease are diagnosed as having juvenile idiopathic arthritis, are female, have a
brown color, and were treated with immunosuppressants.
